Microangiopathy of brain, retina, and inner ear

Author(s): Kitei, R. A., Cafferty, M. S., Odel, J. G., Mitchell, J. P.

Journal/Book: J Neuro-Ophthalmol. 1995; 15: 1185 Ave of the Americas, Journal Subscription Dept, New York, NY 10036. Raven Press. 1-8.

Abstract: Microangiopathy of brain, retina, and inner ear is a rare syndrome manifesting as arteriolar occlusions of the brain, retina, and inner ear, with resultant encephalopathy, visual, and hearing loss. Despite exhaustive laboratory examinations in these patients, no evidence of a systemic disease can be found. We treated and followed an adolescent with this disorder who initially presented with a branch retinal artery occlusion. A unique finding in this case was retinal vessel wall hyperfluorescence noted five days prior to retinal infarction. The patient developed recurrent branch artery occlusions, sensorineural hearing loss, and central nervous system infarctions despite anticoagulation and immunosuppressive treatment.

Note: Article CM Notis, 1044 5TH Ave, New York, NY 10028 USA

Keyword(s): branch retinal artery occlusion; hearing loss; tinnitus; transient ischemic attacks; ARTERIAL-OCCLUSION; ENCEPHALOPATHY

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