Spec Care Dentist. 2002 Jul-Aug; 22(4): 147-50.

General and oral characteristics in Rett syndrome.

MagalhÃ£es MH, Kawamura JY, AraÃºjo LC.

Department of Oral Pathology, School of Dentistry, University of SÃ£o Paulo, SP, Brazil. mhcgmaga@usp.br

Rett syndrome (RS) is a neurodegenerative disorder characterized by developmental arrest of parts of the brain. It is an X chromosome-linked condition which affects females almost exclusively. Recent reports have been generated concerning the multidisciplinary management of individuals exhibiting Rett syndrome. The aim of the present report was to provide an update on the oral manifestations of the disorder. We evaluated the general and oral characteristics of RS in 13 female patients. The most frequent manifestations were stereotyped hand movements and bruxism. The treatment we carried out included the use of biteplanes and acupuncture.